Tumor glómico del septum nasal / Glomic tumor of the nasal septum

Presentamos el caso clínico de una mujer de 58 años que consulta por episodios de epis-taxis autolimitadas por fosa nasal derecha asociados a hipersensibilidad al manipular dicha fosa nasal. A la exploración se evidenció en el septum nasal una lesión mucosa nodular, de consistencia dura y aspecto violáceo. Se llevó a cabo exéresis de la misma por vía endonasal, con resultado histopatológico de tumor glómico (TG) del septum nasal. El TG es una neoplasia benigna perivascular, derivada de las células musculares lisas presentes en el cuerpo glómico; estructura con función termorreguladora, formada por un shunt entre arteriolas y vénulas, sin presencia de red capilar. Los cuerpos glómicos están presentes, mayoritariamente, en extremidades (lecho ungueal). Los tumores glómicos son, verdaderamente, excepcionales en el área ORL, existiendo sólo una treintena de casos publicados hasta la fecha a nivel nasosinusal. La mayoría de casos se presentan entre la 5ᵃ y 6ᵃ década de la vida y más, frecuentemente, en mujeres. Plantea diagnóstico diferencial, fundamentalmente, con dos entidades: el paraganglioma (con el que no debe ser confundido desde el punto de vista terminológico ni histológico), y con el tumor fibroso solitario (antiguo hemangiopericitoma). El comportamiento es benigno y el tratamiento es la cirugía

We present the clinical case of a 58-year-old woman who consulted for episodes of self-limited epistaxis in the right nostril associated with hypersensitivity to manipulation of this nostril. Examination revealed a nodular mucosal lesion in the nasal septum, with a hard consistency and purplish appearance. The lesion was excised endonasally, with histopatho-logical result of a glomus tumor (GT) of the nasal septum. The GT is a benign perivascular neoplasm, derived from smooth muscle cells present in the glomus body; structure with thermoregulatory function, formed by a shunt between arterioles and venules, without the presence of capillary network. Glomus bodies are mostly present in the extremities (nail bed). Glomus tumors are truly exceptional in the ENT area, with only about thirty cases published to date at the nasosinusal level. Most cases occur between the 5th and 6th decade of life and more frequently in women. It raises differential diagnosis fundamentally with two entities: paraganglioma (with which it should not be confused from the terminological or histological point of view) and with solitary fibrous tumor (former hemangiopericytoma). The behavior is benign and the treatment is surgery.

Glomagioma de rodilla / Knee glomangioma

El tumor glómico es una neoplasia benigna poco común que surge del aparato glómico de la piel. Ocurre con mayor frecuencia en los dedos de manos y pies y representa el 1.6% de todos los tumores de tejidos blandos. El diagnóstico clínico puede resultar difícil si el tumor aparece en una ubicación extradigital. Presentamos un caso de tumor glómico de tipo vascular (glomangioma) de localización atípica, suprapatelar externa y de presentación inusual ya que no evidenciaba cambios de color en la superficie, indicando su componente vascular

Glomus tumor are rare benign tumor of the glomus body from the skin. Often occurring in the subungual region and it represents 1.6% of all soft tissue tumors. Clinical diagnosis may result difficult if the tumor occurs in an extra digital location.We report a case of a solitary vascular Glomus Tumor (Glomangioma) with an atypical localization, suprapatellar external and unusual presentation because it did not present with surface color change, indicating the vascular component

Tumor glómico en mucosa bucal: reporte de caso / Tumor in oral mucosa: case report

El tumor glómico es una neoplasia vascular originada de las células del músculo liso del componente neuromioarterial, responsable del control del flujo sanguíneo microvascular. Representa el 1,6% de todos los tumores de tejidos blandos, localizándose principalmente en la zona subungüeal y clínicamente muy doloroso. Su diagnóstico puede ser tardío debido a su pequeño tamaño, manifestaciones clínicas inespecíficas y localizaciones anatómicas inusuales. El tratamiento principalmente es quirúrgico, el cual es curativo, permitiendo además la confirmación histopatológica. Se presenta el reporte de caso de una paciente de 13 años de edad con un tumor glómico de localización inusual en mucosa bucal.

The glomus tumor is a vascular neoplasm originating from smooth muscle cells of neuromyoarterial component, responsible for the control of microvascular blood flow. It represents 1.6% of all soft tissue tumors, being located mainly in the subungual area and clinically very painful. Diagnosis may be delayed because of their small size, nonspecific clinical manifestations and unusual anatomical locations. Treatment is primarily surgical, which is healing, also allowing the histopathologic confirmation. The case report of a 13-year-old patient with an unusual-located glomus tumor in the oral mucosa is presented.

Congenital plaque-like glomangioma: report of two cases

Abstract: Glomus tumors are rare hamartomas that originate from the glomus body. These tumors can be divided into solitary and multiple, the latter also known as glomangioma. We report the case of two patients with a rare variety of glomangioma called congenital plaque-like glomangioma. It presents as numerous red to bluish compressible papules, that increase in size in proportion with the weight and height growth of the child. Diagnostic confirmation is with histopathology and the treatment is surgical.

Type 2 segmental glomangioma - Case report

Glomus tumors originate from modified perivascular muscle cells. The most common form is the solitary one. The multiple form may be associated with dominant genetic inheritance. We report a case of a patient with hemangiomatous lesions on the calcaneus and wrist since birth. In 6 years, there was progression of lesions throughout the body. Multiple glomangiomas are asymptomatic and more common in childhood. They can be confused with other vascular malformations. Histopathological diagnosis is essential. The case shows a type 2 segmental manifestation that can be explained by genetic mutation leading to the loss of heterozygosity. As the child grows, the lesions may disseminate due to mutation in distant parts of the skin. Literature shows few reports. The treatment is conservative.

Malignant Glomus Tumor of the Peritoneum: Case Report

Glomus tumors are usually benign tumors that occur in the skin and soft tissues of the extremities. Visceral locations, such as stomach, intestines or lung, are extremely rare because glomus bodies are rare or absent in these organs. This report describes our experience in a 47-year-old woman diagnosed with a peritoneal malignant glomus tumor. This finding has not been previously reported.

Tumores glómicos de presentación clínica inusual / Unusual clinical presentation of glomus tumors

El tumor glómico es una neoplasia vascular benigna poco común que suele afectar a adultos jóvenes. La localización más frecuente es el lecho ungueal y se caracteriza por dolor paroxístico, sensibilidad localizada e hipersensibilidad a los cambios de temperatura o presión. Comunicamos dos pacientes con presentación clínica inusual. El primer caso corresponde a una paciente de 50 años de edad, con un tumor glómico subungueal de varios meses de evolución sin la clínica característica, lo que dificultó el diagnóstico. Sólo la resonancia magnética permitió visualizar la lesión. La histopatología de la pieza quirúrgicaconfirmó el diagnóstico. El segundo caso hace referencia a una paciente de 61 años que consultó por un tumor doloroso en brazo derecho, sitio inusual para los tumores glómicos...

Synchronous subungual glomus tumors in the same finger / Tumores glômicos subungueais sincrônicos no mesmo dedo

The glomus tumor is an uncommon benign neoplasm of glomus cells. In the majority of the cases it is presented as a solitary painful papule in the subungual region. We report a rare case of a patient with two individual synchronous glomus tumors under the nail bed of the same finger.

O tumor glômico é uma neoplasia benigna de células glômicas. Na maioria dos casos se apresenta como uma pápula solitária dolorosa na região subungueal. Relatamos o caso raro de um paciente com dois tumores glômicos sincrônicos sob o leito ungueal do mesmo dedo.

Primary glomus tumor of the liver: A rare case report and review of the literature.

Glomus tumor is a rare neoplasm of the distal extremities. It occurs very rarely in the deep visceral organs such as stomach, lung, pancreas, ovary, and liver. Herein, we report a very rare case of glomus tumor of the liver in a 50-year-old woman presenting with abdominal mass which was diagnosed after surgery. The tumor was large and cystic; however, the morphology was similar to the ordinary soft-tissue glomus tumor. Tumor cells were reactive with CD34 and SMA. The patient's follow up failed to show any evidence of malignant behavior or tumor recurrence. This report is the third primary glomus tumor of the liver in the English literature.

Gastric Glomus Tumor Showing Hepatic Hemangioma-like Enhancement Pattern on CT / 대한소화기학회지

No abstract available.

Primary glomus tumor of the liver

Primary glomus tumors are extremely rare in the liver. To this date, only two cases of primary glomus tumors of the liver have been reported in the literature. This report is the third case of this specified tumor. The patient was a 50 year-old Iranian woman who presented with a history of epigastric pain and nausea. Abdominal computed tomography [CT] scan showed a huge hepatic mass that replaced the entire left lobe. Surgical biopsy showed that the specimen consisted of a vascular network confined by the proliferation of epithelioid cells with round-to-oval nuclei and eosinophilic cytoplasms. The cells expressed diffuse reactivity for vimentin, smooth muscle actin and CD34, whereas no reactivity was observed with carcinoembryonic antigen, synaptophysin, chromogranin, cytokeratin, and human melanoma black 45. We conclude that glomus tumors must be considered in the differential diagnosis of hepatic masses, with immunohistochemical staining for smooth muscle actin being a useful method to prove the diagnosis

Tumor glômico endobrônquico com atelectasia de lobo superior direito / Bronchial glomus tumor with right upper lobe atelectasis

Tumores glômicos são raras neoplasias benignas de tecidos moles. Relatamos o caso de um paciente de 32 anos de idade que apresentava atelectasia em lobo superior direito devido a um tumor endobrônquico. O paciente foi submetido a lobectomia superior direita e broncoplastia em cunha. O diagnóstico patológico foi de tumor glômico endobrônquico. Até onde sabemos, essa apresentação com atelectasia em lobo superior direito nunca foi relatada. O tumor glômico deve ser considerado no diagnóstico diferencial de lesões endobrônquicas que causam atelectasia lobar.

Glomus tumors are uncommon benign soft tissue neoplasms. We report the case of a 32-year-old male who presented with right upper lobe atelectasis due to an endobronchial tumor. The patient underwent right upper lobectomy and wedge bronchoplasty. The pathological diagnosis was bronchial glomus tumor. To our knowledge, this presentation (with right upper lobe atelectasis) has never before been reported. Glomus tumor should be considered in the differential diagnosis of endobronchial lesions causing lobar atelectasis.

Diagnóstico do tumor glômico pela dermatoscopia do leito e da matriz ungueal / Diagnosis of glomus tumor by nail bed and matrix dermoscopy

A cirurgia é o tratamento definitivo para os tumores glômicos. Algumas vezes, esse procedimento pode representar um desafio, pois, apesar de ser um tumor bem delimitado, a sua visualização pode ser difícil. O uso da dermatoscopia do leito e da matriz ungueal facilita o diagnóstico e auxilia a localização e delimitação do tumor. Trata-se de método simples e de baixo custo que não implica risco adicional ao paciente que irá se submeter a um procedimento cirúrgico.

Surgery is the best treatment for glomus tumors. Sometimes this can be a challenging procedure because, despite being a well-defined tumor, its visualization can be difficult. The use of nail bed and matrix dermoscopy facilitates the diagnosis and aids in the localization and demarcation of the tumor. It is a simple and low-cost procedure that does not involve additional risks to the patient who will undergo surgery.

Glomus en un dedo de la mano Presentación de un caso / Glomus in a finger A case report

El glomus es un tumor benigno de origen vascular más frecuentemente (75% de los casos) localizadoen la región subungueal de los dedos de las manos. Se caracteriza por la tríada de dolor intenso ehipersensibilidad tanto al tacto como a la temperatura. El único tratamiento recomendado es laresección quirúrgica. Con base en el archivo del Departamento de Patología de la Facultad deMedicina de la Universidad de Antioquia, describimos el caso de una mujer de 66 años con este tipode tumor en el cuarto dedo de la mano izquierda; sus características clínicas, radiológicas e histológicasfueron típicas, por lo que constituye un caso muy interesante desde el punto de vista académico.Hacemos una revisión de los aspectos clínicos, diagnósticos y terapéuticos de los pacientes con estetumor. Aunque el cuadro clínico es característico el diagnóstico puede ser difícil si no se tiene presenteesta enfermedad.

Glomus in a finger. A case reportGlomus is a benign tumor of vascular origin, more frequently found in the subungual region of thefingers (75%). It is characterized by the triad of severe pain and hypersensitivity to both touch andtemperature. The only effective treatment is surgical resection. Based on the archives of theDepartment of Pathology, Faculty of Medicine, University of Antioquia (Medellín, Colombia), wedescribe the case of a 66 year-old woman with a glomus in the fourth finger of the left hand. It wastypical from the clinical, radiological and histological points of view, hence its academic interest. Wereview the clinical, diagnostic and therapeutic aspects of patients with this tumor. Despite thecharacteristic history of these patients, diagnosis may be difficult if the tumor is not taken intoaccount.